产品编号：M335000
产品规格：50mg
产品价格：面议
| 标准品编号: | M335000 |
| 名称: | 4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt |
| 别名: | 7-[[2-(Acetylamino)-2-deoxy-6-O-sulfo-β-D-glucopyranosyl]oxy]-4-methyl-2H-1-benzopyran-2-one Monopotassium Salt; MUGS; |
| CAS号: | 210357-38-3 |
| 参考CAS号: | Free Acid: 93751-71-4 |
| 分子式: | C₁₈H₂₀KNO₁₁S |
| 外观: | 白色固体 |
| 熔点: | >148°C (dec.) |
| 分子量: | 497.51 |
| 储存: | Hygroscopic, -20°C Freezer, Under Inert Atmosphere |
| 溶解度: | Water (Slightly) |
| 稳定性: | Hygroscopic |
| 种类: | Standards; Fluorescent Reagents; Carbohydrates and Oligosaccharides; |
| 应用: | A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis. They include Tay Sachs disease, Sandhoff disease and other forms. |
| 参考文献 | |
