4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt

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产品编号:M334715

产品规格:1mg

产品价格:面议


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标准品编号: M334715
名称: 4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt
别名: 4-Methylumbelliferyl α-L-Iduronic Acid-2-sulfate Sodium Salt; 4-Methyl-2-oxo-2H-1-benzopyran-7-yl α-L-Idopyranosiduronic Acid 2-(Hydrogen Sulfate);
CAS号: 1045020-74-3
参考CAS号: 1045348-22-8 free acid
分子式: C₁₆H₁₄Na₂O₁₂S
外观: 白色至白色固体
熔点: >204°C (dec.)
分子量: 476.32
储存: Hygroscopic, -20°C Freezer, Under Inert Atmosphere
溶解度: Methanol (Slightly), Water (Slightly)
稳定性: Hygroscopic
种类: Standards; Fluorescent Reagents; Carbohydrates and Oligosaccharides;
应用: 4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt is a fluorogenic substrate in the assay of α-L-Iduronidase. A fluorimetric enzyme assay for the diagnosis of MPS II (Hunter disease).
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