N-Iso Valerylglycine

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产品编号:I917600

产品规格:1g

产品价格:面议


产品详情

标准品编号: I917600
名称: N-Iso Valerylglycine
别名: N-(3-Methyl-1-oxobutyl)glycine; N-Isovalerylglycine; Isovalerylglycine; N-Isovaleroylglycine;
CAS号: 16284-60-9
分子式: C₇H₁₃NO₃
外观: 白色至白色固体
熔点: 101-104°C
分子量: 159.18
储存: 冰箱
溶解度: DMSO (Slightly), Methanol (Slightly)
种类: Building Blocks; Amino Acids; Pharmaceutical/API Drug Impurities/Metabolites;
应用: N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism.
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