您的位置:对照品 > 标准物质 > 环保部标准物质 >
产品基本信息
产品编号:D454795
产品名称:N-[(3S,4R,5S,6R)-4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate
产品CAS:
规格含量:10mg
产品价格:面议
联系我们:
产品详细介绍
标准品编号:
D454795
名称:
N-[(3S,4R,5S,6R)-4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate
别名:
[3S-(3α,4β,5β,6β)]-N-[4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate; 2-Acetamido-1,5-imino-1,2,5-trideoxy-D-galactitol 6-Sulfate; DGJNAc 6-Sulfate; 2-acetamido-1,2-dideoxy-d-galacto-nojirimycin 6-Sulfate
参考CAS号:
117894-14-1 without salt
分子式:
C₈H₁₆N₂O₇S
分子量:
284.29
种类:
Building Blocks;
应用:
Deficiency of N-[(3S,4R,5S,6R)-4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate sulfatase produces the mucopolysaccharidosis type IV A (MPS IV A, Morquio syndrome type A disease).
参考文献
Olarte, S., et al.: Molecular Genetics and Metabolism, 2, 111 (2014)